What is the 5-year survival rate for patients with untreated ...

[mydiamond]

What is the 5-year survival rate for patients with untreated idiopathic pulmonary artery hyperten-sion (IPAH)?
 
  a. 33
  b. 44
  c. 55
  d. 66

Question 2

What is the most common pulmonary function abnormality found in patients with idiopathic pulmonary artery hypertension (IPAH)?
 
  a. Reduced diffusing capacity of the lungs (DLCO)
  b. Reduced forced vital capacity (FVC)
  c. Reduced forced expiratory flow (FEF25 to 75)
  d. Reduced lung compliance (CL)

[aloop]

Answer to Question 1

ANS: A
IPAH can be life threatening and carries a poor prognosis. Without therapy, only 33 of patients are alive 5 years after the onset of the disorder.

Answer to Question 2

ANS: A
Pulmonary function tests are useful to rule out the presence of significant restrictive or obstruc-tive airway disease. The most common abnormality at pulmonary function testing of patients with IPAH is a low carbon monoxide diffusing capacity (DLCO).