A 4-year-old child has just been diagnosed with ...

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A 4-year-old child has just been diagnosed with pseudohypertrophic (Duchenne) muscular dystrophy. The management plan should include which action?
 
  a. Recommend genetic counseling.
  b. Explain that the disease is easily treated.
  c. Suggest ways to limit use of muscles.
  d. Assist family in finding a nursing facility to provide his care.

Question 2

Latex allergy is suspected in a child with spina bifida. Appropriate nursing interventions include which action?
 
  a. Avoid using any latex product.
  b. Use only nonallergenic latex products.
  c. Administer medication for long-term desensitization.
  d. Teach family about long-term management of asthma.

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Answer to Question 1

ANS: A
Pseudohypertrophic (Duchenne) muscular dystrophy is inherited as an X-linked recessive gene. Genetic counseling is recommended for parents, female siblings, maternal aunts, and their female offspring. No effective treatment exists at this time for childhood muscular dystrophy. Maintaining optimal function of all muscles for as long as possible is the primary goal. It has been found that children who remain as active as possible are able to avoid wheelchair confinement for a longer time. Assisting the family in finding a nursing facility to provide his care is inappropriate at the time of diagnosis. When the child becomes increasingly incapacitated, the family may consider home-based care, a skilled nursing facility, or respite care to provide the necessary care.

Answer to Question 2

ANS: A
Care must be taken that individuals who are at high risk for latex allergies do not come in direct or secondary contact with products or equipment containing latex at any time during medical treatment. There are no nonallergenic latex products. At this time, desensitization is not an option. The child does not have asthma. The parents must be taught about allergy and the risk of anaphylaxis.