A pediatric nurse is educating the client with sickle cell ...

[xroflmao]

A pediatric nurse is educating the client with sickle cell disease and the client's family regarding the genetic implications of the disease. Which information is inappropriate for the nurse to share with the client's family?
 
  A) If both parents have the trait, then with each pregnancy, the risk of having a child with the disease is 50.
  B) The disorder is transmitted as an autosomal recessive genetic defect.
  C) The sickle cell gene may have originated to protect against lethal forms of malaria.
  D) In African-Americans, sickle cell disease occurs in 1 out of every 500 births.

Question 2

An emergency department nurse is caring for a child in a sickle cell crisis. The nurse suspects the etiology of the crisis as being thrombotic in nature due to which clinical manifestations?
 
  Select all that apply.
  A) The client has profound pallor and fatigue.
  B) The client is in extreme pain.
  C) The client has profound hypotension and shock.
  D) The client has a fever.
  E) The client's chest CT reveals a pulmonary infarct.

[Benayers]

Answer to Question 1

Answer: A

In educating the client and the client's parents regarding sickle cell disease, the nurse will state that the disorder is transmitted as an autosomal recessive genetic defect. If both parents have the trait, then with each pregnancy, the risk of having a child with the disease is 25, not 50. The sickle cell gene may have originated to protect against lethal forms of malaria. In African-Americans, sickle cell disease occurs in 1 out of every 500 births.

Answer to Question 2

Answer: B, D

A thrombotic sickle cell crisis is manifested by extreme pain and fever. The client in profound hypotension and shock likely has splenic sequestration as the etiology, not thrombosis. The client with a pulmonary infarct likely has Acute Chest Syndrome, not thrombosis. The client with profound pallor and fatigue likely is in an aplastic crisis, not thrombosis.