A genetic defect diminishing branched-chain alpha-keto acid dehydrogenase (BCKAD) complex activity results in ____.
A) phenylketonuria
B) homocystinuria
C) cystathioninuria
D) maple syrup urine disease
Question 2
A particular amino acid is very important for several metabolic pathways in enterocytes and so it is often added to nutritional mixtures used for hospitalized patients. The important amino acid is ____.
A) tryptophan
B) glutamine
C) glycine
D) asparagine